L81.3: Café au lait spots

The darker colored areas are called café au lait spots because they can look light brown like milky coffee. The skin forms too much pigmentation in the affected areas. If there is too much pigmentation, then the skin in the affected areas will appear darker than normal.

Café au lait spots are evenly colored and have a clearly recognizable edge. They can be roundish and are mainly found on the upper part of the body and on the arms and legs.

If several café au lait spots appear, then this can be evidence of another disease.

Patient Disclaimer

The information provided on this page is for general educational purposes only. It is not intended for self-diagnosis and does not replace professional medical advice. Always consult your doctor or a qualified healthcare provider with any questions or concerns about your health.

If you see an ICD diagnosis code (e.g., on a medical report), be aware that doctors may also include additional indicators to express diagnostic certainty. Only a healthcare professional can interpret these codes accurately in the context of your individual case.

For a complete understanding of your condition and what the diagnosis means for you, please speak directly with your doctor.