E80: Disorders of porphyrin and bilirubin metabolism
E80.5: Crigler-Najjar syndrome
When old blood cells are broken down, bile pigments come into being. These bilirubins are modified by a protein in the liver.
You do not have this protein, or you only have a small amount of it. This condition is congenital, which means you were born with it. If the protein is not working properly, bile pigments will accumulate in the body. The less you have of this protein, the more bile pigments accumulate. That is especially the case when the liver has to do a lot of work. The liver has to work a lot when you drink alcohol or when you have contact with pathogens. As a result, your skin usually looks yellow. Sometimes you may have problems with speaking or hearing.
Patient Disclaimer
The information provided on this page is for general educational purposes only. It is not intended for self-diagnosis and does not replace professional medical advice. Always consult your doctor or a qualified healthcare provider with any questions or concerns about your health.
If you see an ICD diagnosis code (e.g., on a medical report), be aware that doctors may also include additional indicators to express diagnostic certainty. Only a healthcare professional can interpret these codes accurately in the context of your individual case.
For a complete understanding of your condition and what the diagnosis means for you, please speak directly with your doctor.