C96.0: Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis [Letterer-Siwe disease]

The immune system protects the body from pathogens and foreign substances. The immune system can also destroy cells in the body that have pathologically changed. The body's immune system is made up of different types of immune cells. Some immune cells can destroy pathogens or foreign bodies themselves. Other immune cells produce certain antibodies.

In your case, the cancer of specific immune cells developed in a short time. Often you are then suddenly seriously ill. You can then have fever and the lymph nodes in the body can swell up. The lymph nodes are small bean-shaped objects. They are found throughout the body. Lymph nodes filter the tissue fluid. They are part of the defense system. Several organs such as bones, the liver or the lungs are often affected at the same time. The bones of the head or the legs, for example, can be especially destroyed by this cancer. Areas of the skin are usually reddened and flaky. The disease usually develops in infancy.